Dyke-Davidoff-Masson syndrome with crossed cerebellar atrophy.

Acta Neurologica Taiwanica Vol 19 No 2 June 2010 From the Department of Neurology, National Taiwan University Hospital Yun-Lin Branch, Yunlin, Taiwan. Received October 27, 2009. Accepted November 9, 2009. Reprint requests and correspondence to: Fu-Yu Lin, M.D. Department of Neurology, National Taiwan University Hospital Yun-Lin Branch, No. 579, Sec. 2, Yunlin Rd., Douliou City, Yunlin, Taiwan. E-mail: [email protected] A 52-year-old woman was healthy until the age of 5 years when she suffered from a febrile illness with convulsions. Subsequently, she developed shortness of her right upper and lower extremities with weakness. She was able to function as a housewife after marriage with only mild cognitive impairment. She had no history of epilepsy after the above-mentioned febrile episode. A neurological examination revealed facial asymmetry and right spastic hemiparesis with prominent atrophy. Brain magnetic resonance imaging demonstrated left cerebral encephalomalacia with ipsilateral cranial vault thickening, enlargement of the frontal sinuses, and hyperpneumatization. There was right cerebellar atrophy with relative sparing of the middle cerebellar Dyke-Davidoff-Masson Syndrome with Crossed Cerebellar Atrophy